AtresiaThis is an RSS file. You can use it to subscribe to this data in your favourite RSS reader, such as GoogleReader, or to display this data on your own website or blog. Subscribe to this data using MyMedWorm.Subscribe to this data using GoogleReader.Subscribe to this data using Bloglines.Subscribe to this data using MyYahoo.

This page shows you your search results in order of date.

Pages: 1 2 3 4 5 6 7 8 9 10 11 12 13 14 15 16 17 18 19 20 21 22 23 24 25

1226 records returned

Sphenoid sinus development in choanal atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: In unilateral and bilateral choanal atresia patients, there is normal growth of the width of the sphenoid sinuses. (Source: International Journal of Pediatric Otorhinolaryngology)
Source: International Journal of Pediatric Otorhinolaryngology - November 20, 2009 Category: ENT & OMF Authors: Jacques E. Leclerc, Jean Thomas Leclerc Tags: Research papers Source Type: journals

Sialodochostomy as treatment for imperforate submandibular duct: A systematic literature review and report of two casesEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: Congenital floor of mouth cysts arising from imperforate salivary ducts are rare, but they may mimic the appearance of a ranula. Unlike ranulas, these cysts may be safely and effectively cured by simple sialodochostomy. To date, 26 other cases have been described in the literature, and nearly all have been successfully treated with simple incision or marsupialization without recurrence. Care should be taken to exclude ranula as a diagnosis, as incomplete excision may likely result in recurrence. (Source: International Journal of Pediatric Otorhinolaryngology)
Source: International Journal of Pediatric Otorhinolaryngology - November 20, 2009 Category: ENT & OMF Authors: David E. Rosow, Robert F. Ward, Max M. April Tags: Review articles Source Type: journals

Cerebral and cerebellar white matter abnormalities with magnetic resonance imaging in a child with Feingold syndromeEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We present a patient who was found to have areas of cerebral and cerebellar white matter hyperintensity with T2 weighted magnetic resonance (MR) imaging. To the best of our knowledge, this finding has not been previously described. While the significance and pathologic basis of this finding are unknown, its recognition is important since it has potential to be confused with imaging findings in other conditions. Moreover, it is likely to be observed in the future due to increased use of MR imaging. © 2009 Wiley-Liss, Inc. (Source: American Journal of Medical Genetics Part A)
Source: American Journal of Medical Genetics Part A - November 16, 2009 Category: Genetics & Stem Cells Authors: Vance T. Lehman, Marc C. Patterson, Dusica Babovic-Vuksanovic, Charlotte Rydberg Source Type: journals

Usefulness of a scoring system in the interpretation of histology in neonatal cholestasis.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
CONCLUSION: A 7-feature, 15-point histological scoring system had good diagnostic accuracy in the interpretation of liver histology in neonatal cholestasis. PMID: 19908342 [PubMed - in process] (Source: World Journal of Gastroenterology : WJG)
Source: World Journal of Gastroenterology : WJG - November 13, 2009 Category: Gastroenterology Authors: Lee WS, Looi LM Tags: World J Gastroenterol Source Type: journals

[Seminar] Biliary atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Biliary atresia is a rare disease of infancy, which has changed within 30 years from being fatal to being a disorder for which effective palliative surgery or curative liver transplantation, or both, are available. Good outcomes for infants depend on early referral and timely Kasai portoenterostomy, and thus a high index of suspicion is needed for investigation of infants with persistent jaundice. In centres with much experience of treating this disorder, up to 60% of children will achieve biliary drainage after Kasai portoenterostomy and will have serum bilirubin within the normal range within 6 months. 80% of children wh...
Source: LANCET - November 13, 2009 Category: Journals (General) Authors: Jane L Hartley, Mark Davenport, Deirdre A Kelly Tags: Seminar Source Type: journals

The illusion of severe carpal tunnel syndrome (CTS)Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
In this report we present a young woman with mild bilateral CTS, based on electrophysiological studies, in whom marked thenar atrophy was on a congenital basis related to the VATER association (vertebral anomalies, anal atresia, tracheoesophageal fistula, and radial or renal abnormalities). Muscle Nerve, 2010 (Source: Muscle and Nerve)
Source: Muscle and Nerve - November 13, 2009 Category: Internal Medicine Authors: Ludwig Gutmann, Christopher Nance Source Type: journals

The primordial pool of follicles and nest breakdown in mammalian ovariesEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
The creation of the pool of follicles available for selection and ovulation is a multi-faceted, tightly regulated process that spans the period from embryonic development through to the first reproductive cycle of the organism. In mice, this development can occur in mere weeks, but in humans, it is sustained for years. Embryonic germ cell development involves the migration of primordial germs cells to the genital ridge, and the mitotic division of germ cell nuclei without complete cytokinesis to form a multi-nucleated syncytia, or germ cell nest. Through combined actions of germ cell apoptosis and somatic cell migration, t...
Source: Molecular Human Reproduction - November 12, 2009 Category: Molecular Biology Authors: Tingen, C., Kim, A., Woodruff, T. K. Tags: New Research Horizon Reviews Source Type: journals

Health-related quality of life and its determinants in children and adolescents born with oesophageal atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusion: In this first study describing health-related quality of life in children and adolescents born with oesophageal atresia, we demonstrated that general health remains impaired because of a high incidence of concomitant anomalies and gastrointestinal symptoms in patients with oesophageal atresia when compared with the healthy reference population. (Source: Acta Paediatrica)
Source: Acta Paediatrica - November 12, 2009 Category: Pediatrics Authors: MG Peetsold, HA Heij, JA Deurloo, RJBJ Gemke Source Type: journals

The complete three-vessel view in prenatal detection of congenital heart defectsEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
To evaluate the effectiveness of the complete three-vessel view (c3VV) in assessment of fetuses with prenatally diagnosed congenital heart defects (CHD).Fetuses with prenatal suspicion of CHD were prospectively recruited into the study. All examinations included a c3VV for assessment of abnormalities in alignment, arrangement, vessel size, number of vessels, aortic arch sidedness and color flow mapping. Definite diagnoses of CHD were based on neonatal cardiologic exams or postnatal autopsy.Of 106 consecutive fetuses with CHD, 75 were shown to have at least one abnormality on the c3VV, a detection rate of 70.8%. When septal...
Source: Prenatal Diagnosis - November 12, 2009 Category: Perinatology & Neonatology Authors: Theera Tongsong, Fuanglada Tongprasert, Kasemsri Srisupundit, Suchaya Luewan Source Type: journals

Childhood Esophageal Atresia Linked to Adult ScoliosisEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Adults with a history of esophageal atresia repair during infancy face a substantially higher risk of scoliosis, according to research published online Nov. 9 in Pediatrics. (Source: Modern Medicine)
Source: Modern Medicine - November 12, 2009 Category: Journals (General) Source Type: info

Atresia of ileocecal junction, ileocecal valve: Rare variants of bowel atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We report two such cases. Radiology showed dilated ileal segment and distal micro colon in both the cases. At laparotomy there was atresia of ileocecal junction in the first case and isolated ileocaecal valve atresia with normal ileocecal junction in the other case. Both the babies were managed by ileocolic resection with an end to end anastomosis. The prognosis of ileocecal atresias is satisfactory. (Source: Journal of Indian Association of Pediatric Surgeons)
Source: Journal of Indian Association of Pediatric Surgeons - November 10, 2009 Category: Surgery Authors: Srivastava Punit, Gangopadhyay A N, Gupta D K, Sharma S P, Upadhyaya Vijay D, Kumar Vijayendra, Jaiman Richa Source Type: journals

Tetralogy of Fallot with Persistent Fifth Aortic Arch: Echocardiographic DiagnosisEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This report describes a new case of P5A in an infant with tetralogy of Fallot but not pulmonary atresia, which was diagnosed echocardiographically. The echo-Doppler characteristics of P5A in the presence of right ventricular outflow obstruction are described, and the implications regarding surgery for the accompanying defects are discussed. To the authors’ best knowledge, the described case is the first reported instance of P5A in this specific setting. Content Type Journal ArticleCategory Case ReportDOI 10.1007/s00246-009-9573-4Authors Gerard Holmes, Pediatrix Cardiology Associates of New Mexico 201 Cedar SE, S...
Source: Pediatric Cardiology - November 10, 2009 Category: Cardiology Tags: Pediatric Cardiology Source Type: journals

Two Multivitamin Preparations Ineffective for Biliary AtresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Commonly used multivitamin supplements containing fat-soluble vitamins fail to prevent fat-soluble vitamin deficiencies. Medscape Medical News (Source: Medscape PublicHealth Headlines)
Source: Medscape PublicHealth Headlines - November 4, 2009 Category: Primary Care Tags: Critical Care Source Type: info

Great vessel development requires biallelic expression of Chd7 and Tbx1 in pharyngeal ectoderm in miceEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Aortic arch artery patterning defects account for approximately 20% of congenital cardiovascular malformations and are observed frequently in velocardiofacial syndrome (VCFS). In the current study, we screened for chromosome rearrangements in patients suspected of VCFS, but who lacked a 22q11 deletion or TBX1 mutation. One individual displayed hemizygous CHD7, which encodes a chromodomain protein. CHD7 haploinsufficiency is the major cause of coloboma, heart defect, atresia choanae, retarded growth and development, genital hypoplasia, and ear anomalies/deafness (CHARGE) syndrome, but this patient lacked the major diagnosti...
Source: Journal of Clinical Investigation - November 3, 2009 Category: Biomedical Science Authors: Victoria Randall, Karen McCue, Catherine Roberts, Vanessa Kyriakopoulou, Sarah Beddow, Angela N. Barrett, Francesca Vitelli, Katrina Prescott, Charles Shaw-Smith, Koen Devriendt, Erika Bosman, Georg Steffes, Karen P. Steel, Subreena Simrick, M. Albert Bas Source Type: journals

ARTICLE: Antibacterial Medication Use During Pregnancy and Risk of Birth Defects: National Birth Defects Prevention StudyEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions Reassuringly, penicillins, erythromycins, and cephalosporins, although used commonly by pregnant women, were not associated with many birth defects. Sulfonamides and nitrofurantoins were associated with several birth defects, indicating a need for additional scrutiny. (Source: Archives of Pediatrics)
Source: Archives of Pediatrics - November 2, 2009 Category: Pediatrics Authors: Crider, K. S., Cleves, M. A., Reefhuis, J., Berry, R. J., Hobbs, C. A., Hu, D. J. Tags: Pediatrics, Congenital Malformations, Women's Health, Pregnancy and Breast Feeding, Drug Therapy, Adverse Effects Article Source Type: journals

Antibacterial Medication Use During Pregnancy and Risk of Birth Defects: National Birth Defects Prevention Study [Article]Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions Reassuringly, penicillins, erythromycins, and cephalosporins, although used commonly by pregnant women, were not associated with many birth defects. Sulfonamides and nitrofurantoins were associated with several birth defects, indicating a need for additional scrutiny. (Source: Archives of Pediatrics)
Source: Archives of Pediatrics - November 2, 2009 Category: Pediatrics Authors: Crider, K. S., Cleves, M. A., Reefhuis, J., Berry, R. J., Hobbs, C. A., Hu, D. J. Tags: Pediatrics, Congenital Malformations, Women's Health, Pregnancy and Breast Feeding, Drug Therapy, Adverse Effects Article Source Type: journals

Neonatal hemochromatosis and Martinez-Frias syndrome of intestinal atresia and diabetes mellitus in a consanguineous newborn.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We report on a newborn from consanguineous parents who presented with multiple congenital anomalies and neonatal hemochromatosis. The syndrome consisted of intrauterine growth retardation, intestinal atresia, gallbladder aplasia and diabetes mellitus, and fitted with the diagnosis of Martinez-Frias syndrome, a very rare autosomal recessive phenotype, the gene of which remains to be identified. We suggest that neonatal hemochromatosis may be part of the Martinez-Frias syndrome. Molecular analyses in this and other reported patients with the Martinez-Frias syndrome should shed light on gut development and iron metabolism. ...
Source: European Journal of Medical Genetics - October 31, 2009 Category: Genetics & Stem Cells Authors: Martinovici D, Ransy V, Eijnden SV, Ridremont C, Pardou A, Cassart M, Avni F, Donner C, Lingier P, Mathieu A, Gulbis B, De Brouckère V, Cnop M, Abramowicz M, Désir J Tags: Eur J Med Genet Source Type: journals

Outcomes in Neonates with Gastroschisis in U.S. Children's HospitalsEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We examined descriptive characteristics and conducted multivariate regression models examining risk factors for mortality, during the birth hospitalization, and sepsis. Analysis of 2490 neonates with gastroschisis found 90 deaths (3.6%) and sepsis in 766 (31%). Critical comorbidities and procedures are cardiovascular defects (15%), pulmonary conditions (5%), intestinal atresia (11%), intestinal resection (12.5%), and ostomy formation (8.3%). Factors associated with mortality were large bowel resection (odds ratio [OR] 8.26, 95% confidence interval [CI] 1.17 to 58.17), congenital circulatory (OR 5.62, 95% CI 2.11 to 14.91),...
Source: American Journal of Perinatology - October 29, 2009 Category: Perinatology & Neonatology Source Type: journals

Congenital mitral regurgitation due to papillary muscle infarction: a case report and approach to evaluationEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We report a case of congenital atresia of left main coronary artery in an asymptomatic 8-month-old presenting with an incidental finding of mitral valvar regurgitation. Appropriate investigations and management lead to restoration of normal coronary blood flow and valve function. This particular case illustrates that congenital coronary anomalies may present in an otherwise asymptomatic child. It should be considered as one of the possible differential diagnosis in unexplained mitral regurgitation. Early recognition and prompt surgical treatment can radically modify the prognosis. Content Type Journal ArticleCatego...
Source: European Journal of Pediatrics - October 27, 2009 Category: Pediatrics Tags: European Journal of Pediatrics Source Type: journals

Anomalous Origin of a Coronary Artery from the Right Branchiocephalic Trunk Associated with Complex Congenital Heart DiseaseEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This report describes the extremely rare case of a 42-day-old boy with anomalous origin of a single coronary artery from the right branchiocephalic trunk associated with hypoplastic left ventricle, mitral atresia, truncus arteriosus, total anomalous pulmonary venous drainage, and patent foramen ovale. Content Type Journal ArticleCategory Images in Pediatric CardiologyDOI 10.1007/s00246-009-9561-8Authors Fang Liu, Pediatric Heart Center, Children’s Hospital of Fudan University Shanghai ChinaGuoying Huang, Pediatric Heart Center, Children’s Hospital of Fudan University Shanghai ChinaJing Zhang, Pediatric Heart Cen...
Source: Pediatric Cardiology - October 27, 2009 Category: Cardiology Tags: Pediatric Cardiology Source Type: journals

Regression of a Coronary Arterial Fistula in an Infant with Pulmonary Atresia and an Intact Ventricular SeptumEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This report describes a premature newborn with pulmonary atresia and an intact ventricular septum who presented with a significant fistula between the right ventricle and the left anterior descending coronary artery (LAD). The right ventricle was not decompressed to prevent myocardial damage. After 2 months, the fistula had closed spontaneously. The pulmonary valve was opened, and biventricular circulation was achieved. Content Type Journal ArticleCategory Case ReportDOI 10.1007/s00246-009-9559-2Authors Anca Popoiu, Deutsches Herzzentrum München Department of Pediatric Cardiology and Congenital Heart Disease ...
Source: Pediatric Cardiology - October 27, 2009 Category: Cardiology Tags: Pediatric Cardiology Source Type: journals

Fgf10 gene expression is delayed in the embryonic lung mesenchyme in the adriamycin mouse modelEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusion Delayed Fgf10 gene expression during the critical period of separation of the trachea and esophagus may affect lung bud formation in the adriamycin model leading to tracheoesophageal malformations. Content Type Journal ArticleCategory Original ArticleDOI 10.1007/s00383-009-2519-3Authors Piotr Hajduk, Our Lady’s Children’s Hospital Children’s Research Centre Crumlin Dublin 12 IrelandPaula Murphy, Trinity College, University of Dublin Department of Zoology Dublin 2 IrelandPrem Puri, Our Lady’s Children’s Hospital Children’s Research Centre Crumlin Dublin 12 Ireland Journal P...
Source: Pediatric Surgery International - October 23, 2009 Category: Surgery Tags: Pediatric Surgery International Source Type: journals

Prenatal presentation and postnatal management of congenital thoracic malformationsEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Abstract: The antenatal finding of a congenital thoracic malformation (CTM) leads to anxiety in the parents and uncertainty as to the optimal management. The antenatal spectrum of CTM includes congenital cystic adenomatoid malformation, sequestration, congenital lobar emphysema, enteric and bronchogenic cysts, and bronchial atresia. Most lesions require no antenatal intervention, and shrink substantially in the third trimester, but if fetal hydrops develops, then antenatal intervention is required, occasionally medical but more usually surgical, because mortality is high. If the baby is symptomatic in the newborn period, t...
Source: Early Human Development - October 23, 2009 Category: Perinatology & Neonatology Authors: Andrew Bush Tags: Guest Editor N. Modi Source Type: journals

Epidemiology of biliary atresia in England and Wales (1999-2006)Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: There is a remarkable variation of incidence of biliary atresia within England and Wales, some of which may have been caused by factors related to a different aetiological and racial background. (Source: Archives of Disease in Childhood - Fetal and Neonatal Edition)
Source: Archives of Disease in Childhood - Fetal and Neonatal Edition - October 21, 2009 Category: Perinatology & Neonatology Authors: Livesey, E, Borja, M C., Sharif, K, Alizai, N, McClean, P, Kelly, D, Hadzic, N, Davenport, M Tags: Pancreas and biliary tract Original articles Source Type: journals

Vitamin K deficiency bleeding in cholestatic infants with alpha-1-antitrypsin deficiencyEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: The risk of VKD bleeding in breastfed infants with A1AD was high and did not correlate with serum level of conjugated bilirubin at diagnosis. A similar absolute risk was previously reported in breastfed infants with biliary atresia under the same prophylactic regimen. This confirms that—without adequate prophylaxis—the risk of VKD bleeding is uniformly high in exclusively breastfed infants with cholestatic jaundice, irrespective of underlying aetiology. (Source: Archives of Disease in Childhood - Fetal and Neonatal Edition)
Source: Archives of Disease in Childhood - Fetal and Neonatal Edition - October 21, 2009 Category: Perinatology & Neonatology Authors: van Hasselt, P M, Kok, K, Vorselaars, A D M, van Vlerken, L, Nieuwenhuys, E, de Koning, T J, de Vries, R A, Houwen, R H J Tags: Pancreas and biliary tract, Childhood nutrition, Malnutrition, Reproductive medicine, Infant nutrition (including breastfeeding), Rheumatology Original articles Source Type: journals

Unifocalization of major aortopulmonary collateral arteries in pulmonary atresia with ventricular septal defect is essential to achieve excellent outcomes irrespective of native pulmonary artery morphologyEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusion: By using a strategy of unifocalization, intrapericardial pulmonary artery reconstruction, and right ventricle-pulmonary artery conduit, excellent long-term survival can be achieved in this group of patients even in the absence of native intrapericardial pulmonary arteries. (Source: The Journal of Thoracic and Cardiovascular Surgery)
Source: The Journal of Thoracic and Cardiovascular Surgery - October 21, 2009 Category: Cardiovascular & Thoracic Surgery Authors: Ben Davies, Shafi Mussa, Paul Davies, John Stickley, Timothy J. Jones, David J. Barron, William J. Brawn Tags: Congenital Heart Disease Source Type: journals

Clinical Trial Simulations in Pediatric Patients Using Realistic Covariates: Application to Teduglutide, a Glucagon-Like Peptide-2 Analog in Neonates and Infants With Short-Bowel Syndrome.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This report details the application of clinical trial simulations coupled with a novel approach using generalized additive modeling for location, scale, and shape (GAMLSS) that facilitates the simulation of demographic covariates specific to the targeted patient populations. The goal was to optimize phase I dosing strategies and the likelihood of achieving target exposure and therapeutic effect. PMID: 19847163 [PubMed - as supplied by publisher] (Source: Clinical Pharmacology and Therapeutics)
Source: Clinical Pharmacology and Therapeutics - October 20, 2009 Category: Drugs & Pharmacology Authors: Mouksassi MS, Marier JF, Cyran J, Vinks AA Tags: Clin Pharmacol Ther Source Type: journals

Comparison of Impact of Prenatal Versus Postnatal Diagnosis of Congenitally Corrected Transposition of the Great ArteriesEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
In conclusion, CCTGA has a >70% risk of intervention in the first 3 years after birth. The outlook is guarded and has an important effect on prenatal counseling. (Source: The American Journal of Cardiology)
Source: The American Journal of Cardiology - October 20, 2009 Category: Cardiology Authors: Andrea W. Wan, Alexandra Jevremovic, Elif Seda Selamet Tierney, Brian W. McCrindle, Elizabeth Dunn, Cedric Manlhiot, Rachel M. Wald, John P. Kingdom, Edgar T. Jaeggi, Lynne E. Nield Tags: Congenital Heart Disease Source Type: journals

The potential of disproportionate growth of tricuspid valve after decompression of the right ventricle in patients with pulmonary atresia and intact ventricular septaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: Disproportional growth of the tricuspid valve can occur, especially in patients with small tricuspid valves and lower right ventricular pressures after decompression. The findings support the possibility of neonates with small tricuspid valves undergoing biventricular repair after right ventricular decompression surgery. (Source: The Journal of Thoracic and Cardiovascular Surgery)
Source: The Journal of Thoracic and Cardiovascular Surgery - October 19, 2009 Category: Cardiovascular & Thoracic Surgery Authors: Shu-Chien Huang, Kozo Ishino, Shingo Kasahara, Ko Yoshizumi, Yasuhiro Kotani, Shunji Sano Tags: Congenital Heart Disease Source Type: journals

Journal Scan: Long-Term Results of Catheter-Based Treatment of Pulmonary Atresia and Intact Ventricular Septum (Heart 2009;95:1520-1524.)Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
A retrospective review of neonates with PAIVS was performed at a single center. Exclusion criteria included right ventricular dependent coronary circulation, hypoplastic monopartite right ventricle, and severe Ebstein anomaly of the tricuspid valve. (Source: Cardiosource)
Source: Cardiosource - October 16, 2009 Category: Cardiology Source Type: organizations

Radiofrequency perforation of the pulmonary valve in an adult with tetralogy of Fallot and pulmonary atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
MiscellaneousArif Anis Khan, Michael J Mullen, Alan G Magee, Cardiology in the Young, Volume 19 Issue 05 , pp 517-518Abstract (Source: Cardiology in the Young)
Source: Cardiology in the Young - October 14, 2009 Category: Cardiology Source Type: journals

Pulmonary atresia with intact ventricular septum associated with aortic coarctationEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We describe a patient having pulmonary atresia with intact septum associated with aortic coarctation, which to the best of our knowledge has been previously described on but one occasion. (Source: Cardiology in the Young)
Source: Cardiology in the Young - October 14, 2009 Category: Cardiology Source Type: journals

Clinical application of fetal urine production rate in unexplained polyhydramniosEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
To evaluate the clinical use of hourly fetal urine production rate (HFUPR) in polyhydramnios.This was a retrospective review of 33 singleton pregnancies with polyhydramnios, 30 of them unexplained and three due to gastrointestinal atresia. HFUPR was estimated using three-dimensional ultrasound and was compared with recently established nomograms. Abnormal midterm outcome, defined as diagnosis or persistence of pathology after the neonatal period until the age of 2 years, was analyzed according to prenatal HFUPR measurements and other polyhydramnios characteristics.Seventeen of the 30 fetuses with unexplained polyhydramnios...
Source: Ultrasound in Obstetrics and Gynecology - October 13, 2009 Category: Radiology Authors: C. Touboul, O. Picone, J. M. Levaillant, C. Boithias, R. Frydman, M. Boulvain, M. V. Senat Source Type: journals

Clinical application of fetal urine production rate in unexplained polyhydramnios.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
CONCLUSION: HFUPR was associated with the mechanism of polyhydramnios but failed to help in the prognosis of unexplained polyhydramnios because of lack of power. Children with prenatal unexplained polyhydramnios and HFUPR above the 95(th) centile should nevertheless receive detailed pediatric follow-up. Copyright (c) 2009 ISUOG. Published by John Wiley & Sons, Ltd. PMID: 19830790 [PubMed - as supplied by publisher] (Source: The Ultrasound Review of Obstetrics and Gynecology)
Source: The Ultrasound Review of Obstetrics and Gynecology - October 13, 2009 Category: Radiology Authors: Touboul C, Picone O, Levaillant JM, Boithias C, Frydman R, Boulvain M, Senat MV Tags: Ultrasound Obstet Gynecol Source Type: journals

The Benefits of High-flow Management in Children With Pulmonary AtresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
The high-flow management of cardiopulmonary bypass (CPB; [ge]2.4 L/min/m2) is a standard strategy used at this institute for children with pulmonary atresia (PA) due to a fear that the blood flow may be diverted by the major/minor aortopulmonary-collateral-arteries and hypervascularization due to long-term hypoxia. The purpose of this study was to describe the validity of high-flow management in children with PA. The CPB records of 23 children with PA who underwent a definitive biventricular repair between Feb 2006 and Nov 2008 were retrospectively reviewed. The mean age at the operation was 33 ± 22 months. The blood-pres...
Source: Artificial Organs - October 9, 2009 Category: Transplant Surgery Authors: Yasuhiro Fujii, Yasuhiro Kotani, Takuya Kawabata, Shinya Ugaki, Shigeru Sakurai, Hironori Ebishima, Hideshi Itoh, Mahito Nakakura, Sadahiko Arai, Shingo Kasahara, Shunji Sano, Tatsuo Iwasaki, Yuichiro Toda Source Type: journals

Genetic factors in esophageal atresia, tracheo-esophageal fistula and the VACTERL association: Roles for FOXF1 and the 16q24.1 FOX transcription factor gene cluster, and review of the literature.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This article reviews these new data alongside other genetic causes of syndromic esophageal atresia, and also highlights information from relevant mouse models, particularly those for genes in the Sonic Hedgehog pathway. PMID: 19822228 [PubMed - as supplied by publisher] (Source: European Journal of Medical Genetics)
Source: European Journal of Medical Genetics - October 8, 2009 Category: Genetics & Stem Cells Authors: Shaw-Smith C Tags: Eur J Med Genet Source Type: journals

Embryology and Epidemiology of MicrotiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Facial plast Surg 2009; 25: 145-148DOI: 10.1055/s-0029-1239444ABSTRACTThe auricle derives from six hillocks arising from the first and second branchial arches. Different hillocks give rise to different parts of the pinna. In the course of embryonic development, the auricle migrates postero-cranially as the mandible enlarges. Auricular malformations, such as microtia, are thought to be related to cell death of the first and second arch derivatives. The prevalence and characteristics of microtia vary in different populations. The prevalence ranges from 0.83 to 17.4 per 10,000. Microtia is more common in males, and right-side...
Source: Facial Plastic Surgery - October 7, 2009 Category: Cosmetic Surgery Source Type: journals

To Breed or not to Breed: Physiological Correlates of Reproductive Status in a Facultatively Biennial Iguanid.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
It is unusual for seasonal breeders to frequently skip opportunities for reproduction. We investigated the relationship between physiological state and reproductive decision-making in Galápagos marine iguanas (Amblyrhynchus cristatus), a species in which females typically reproduce biennially, although the proportion of breeding individuals varies significantly across years. Nearly all adult-sized females initiated follicular development prior to the lekking period, but 38% of females resorbed all developing follicles 5-15 days before the start of copulations. Receptive and non-receptive females differed in reprod...
Source: Hormones and Behavior - October 5, 2009 Category: Endocrinology Authors: Vitousek MN, Mitchell MA, Romero LM, Awerman J, Wikelski M Tags: Horm Behav Source Type: journals

Congenital unilateral intranasal membranous septa with choanal atresia dividing the nasal cavity into two blind pouch: A case reportEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
(Source: International Journal of Pediatric Otorhinolaryngology)
Source: International Journal of Pediatric Otorhinolaryngology - October 5, 2009 Category: ENT & OMF Tags: Abstracts Source Type: journals

Caring for a post-surgical neonate with choanal atresia.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
This case study illustrates a nursing care pathway for a neonate with choanal atresia. The article highlights the main issues and best practice involved in safely and effectively maintaining a clear airway while being aware of the needs of a premature infant. It also discusses the emotional and practical needs of the family. PMID: 19886565 [PubMed - in process] (Source: Paediatric Nursing)
Source: Paediatric Nursing - October 1, 2009 Category: Nursing Authors: Aspin A, McNicholas K Tags: Paediatr Nurs Source Type: journals

Surgical outcomes of esophageal atresia without fistula for 24 years at a single institutionEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Conclusions: Management of EA without fistula remains challenging. Most patients required staged treatment that included esophageal replacement. The frequency of late complications indicates the need for programmed long-term review. (Source: Journal of Pediatric Surgery)
Source: Journal of Pediatric Surgery - September 30, 2009 Category: Surgery Authors: Andrew J.A. Holland, Ori Ron, Agostino Pierro, David Drake, Joseph I. Curry, Edward M. Kiely, Lewis Spitz Tags: Original Articles Source Type: journals

Intrauterine intussusception: a rare cause of intestinal atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We report a case of ileal atresia owing to antenatal intussusception revealed as an intraluminal polypoid lesion after surgical intervention. (Source: Journal of Pediatric Surgery)
Source: Journal of Pediatric Surgery - September 30, 2009 Category: Surgery Authors: Carlos Pueyo, Joaquín Maldonado, Yolanda Royo, Robert Skrabski, Ida Di Crosta, Antoni Raventós Tags: Case Reports Source Type: journals

An extremely rare abnormality of a double tracheoesophageal fistula without atresia of the esophagus; a case report and review of the literatureEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Abstract: Tracheoesophageal fistulas without atresia of the esophagus are rare abnormalities of the upper gastrointestinal tract with an incidence rate of between 1% and 5%. Even more infrequent are 2 tracheoesophageal fistulas without atresia of the esophagus. This case report illustrates the history of an infant with 2 tracheoesophageal fistulas. The corresponding literature was reviewed, and a diagnostic algorithm was described. (Source: Journal of Pediatric Surgery)
Source: Journal of Pediatric Surgery - September 30, 2009 Category: Surgery Authors: Tobias Schulte, Tobias Ankermann, Andreas Claas, Silvia Engler Tags: Journal of Pediatric Surgery Electronic Pages (Available only online at www.jpedsurg.org) Source Type: journals

Congenitally Closed Tricuspid Annulus Functions as Arrhythmogenic Substrate of Atrial Arrhythmia in Patient with Tricuspid AtresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
We report that a congenitally closed tricuspid annulus is one of the anatomical obstacles when we consider atrial tachyarrhythmia. (PACE 2009; e1[ndash]e3) (Source: Pacing and Clinical Electrophysiology : PACE)
Source: Pacing and Clinical Electrophysiology : PACE - September 29, 2009 Category: Cardiology Authors: HEIMA SAKAGUCHI, AYA MIYAZAKI, TAKUYA HIRATA, KAZUHIRO SATOMI Source Type: journals

Subfertility Caused by Altered Follicular Development and Oocyte Growth in Female Mice Lacking PKBalpha/Akt1.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Mammalian females are endowed with a finite number of primordial follicles at birth. Immediately following formation of the primordial follicle pool, cohorts of follicles are either culled from the ovary or are recruited to grow until the primordial follicle population is depleted. The majority of ovarian follicles including the oocytes undergo atresia through apoptotic cell death. As PKBalpha/Akt1 is known to regulate apoptosis, we asked whether Akt1 functioned in the regulation of folliculogenesis in the ovary. Akt1-/- females display reduced fertility and abnormal estrous cyclicity. At Postnatal Day 25, Akt1-/- ovar...
Source: Biology of Reproduction - September 29, 2009 Category: Reproduction Medicine Authors: Brown C, Larocca J, Pietruska J, Ota M, Anderson L, Duncan Smith S, Weston P, Rasoulpour T, Hixon ML Tags: Biol Reprod Source Type: journals

An extraordinary cause of ischemic chest pain in a young man: Congenital ostial atresia of the right coronary artery.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Chest pain in a young person without cardiovascular risk factors is usually attributed to noncoronary causes; however, if the history suggests ischemic pain, the potential presence of unusual cardiovascular abnormalities should not be disregarded. The present case describes a young man with solitary congenital ostial atresia of right coronary artery, who to our knowledge is only the second case in the medical literature. Manifestation of ischemic symptoms in a relatively advanced age in patients with coronary artery atresia may mislead clinicians to interpret them as signs of atherosclerotic coronary artery disease. Th...
Source: Journal of Cardiology - September 29, 2009 Category: Cardiology Authors: Karadag B, Ayan F, Ismailoglu Z, Goksedef D, Ataev Y, Vural VA Tags: J Cardiol Source Type: journals

The case for fetal cardiac intervention [Reviews]Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Surgery for congenital heart disease is now often performed in the first months of life because mortality is higher and myocardial damage more serious in unoperated children or those undergoing delayed surgery. Fetal cardiac intervention may prove a logical extension and has been proposed for fetuses with critical semilunar valve stenosis or atresia. Early ventricular decompression may halt disease progression, alter the natural history and improve postnatal outcomes either by preserving a two-ventricle circulation or by improving the outlook for single-ventricle candidates because of a healthier myocardium and pulmonary b...
Source: Heart - September 28, 2009 Category: Cardiology Authors: Gardiner, H M Tags: Reviews Source Type: journals

Genetics Home Reference: epidermolysis bullosa with pyloric atresiaEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
New topic on Genetics Home Reference (Source: NLM General Announcements)
Source: NLM General Announcements - September 28, 2009 Category: Databases & Libraries Authors: NLM Source Type: organizations

[Reviews] The case for fetal cardiac interventionEmail this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Surgery for congenital heart disease is now often performed in the first months of life because mortality is higher and myocardial damage more serious in unoperated children or those undergoing delayed surgery. Fetal cardiac intervention may prove a logical extension and has been proposed for fetuses with critical semilunar valve stenosis or atresia. Early ventricular decompression may halt disease progression, alter the natural history and improve postnatal outcomes either by preserving a two-ventricle circulation or by improving the outlook for single-ventricle candidates because of a healthier myocardium and pulmonary b...
Source: Heart - September 27, 2009 Category: Cardiology Authors: Gardiner, H M Tags: Reviews Source Type: journals

The morphological classification of bovine ovarian follicles.Email this article to a colleague. Save this article to My Clippings. Discuss or comment on this article.
Follicle classification is an important aid to the understanding of follicle development and atresia. Some bovine primordial follicles have the classical primordial shape, but ellipsoidal shaped follicles with some cuboidal granulosa cells at the poles are far more common. Preantral follicles have one of two basal lamina phenotypes, either a single aligned layer or one with additional layers. In antral follicles <5 mm diameter half the healthy follicles have columnar shaped basal granulosa cells additional layers of basal lamina that appear as loops in cross section ('loopy'). The remainder have an aligned single-la...
Source: Reproduction - September 27, 2009 Category: Reproduction Medicine Authors: Rodgers RJ, Irving-Rodgers HF Tags: Reproduction Source Type: journals